ASPH (aspartate beta-hydroxylase)

2003-02-01  

Identity

HGNC
LOCATION
8q12.3
LOCUSID
ALIAS
AAH,BAH,CASQ2BP1,FDLAB,HAAH,JCTN,junctin
FUSION GENES

Other Information

Locus ID:

NCBI: 444
MIM: 600582
HGNC: 757
Ensembl: ENSG00000198363

Variants:

dbSNP: 444
ClinVar: 444
TCGA: ENSG00000198363
COSMIC: ASPH

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000198363ENST00000356457Q12797
ENSG00000198363ENST00000379449Q12797
ENSG00000198363ENST00000379454Q12797
ENSG00000198363ENST00000389204Q12797
ENSG00000198363ENST00000445642Q12797
ENSG00000198363ENST00000517661G3XAN5
ENSG00000198363ENST00000517847Q12797
ENSG00000198363ENST00000517856E5RHJ2
ENSG00000198363ENST00000517903Q12797
ENSG00000198363ENST00000518068Q12797
ENSG00000198363ENST00000518306E5RG29
ENSG00000198363ENST00000519234E5RG56
ENSG00000198363ENST00000519264A0A087WW05
ENSG00000198363ENST00000519678A0A087X0J4
ENSG00000198363ENST00000522349E5RHK2
ENSG00000198363ENST00000522603Q12797
ENSG00000198363ENST00000522835Q12797
ENSG00000198363ENST00000522919E5RJL3
ENSG00000198363ENST00000523927A0A087WUJ2
ENSG00000198363ENST00000524173A0A087WW51
ENSG00000198363ENST00000541428Q12797

Expression (GTEx)

0
10
20
30
40
50
60
70
80
90
100

Pathways

PathwaySourceExternal ID
Muscle contractionREACTOMER-HSA-397014
Transmembrane transport of small moleculesREACTOMER-HSA-382551
Ion channel transportREACTOMER-HSA-983712
Stimuli-sensing channelsREACTOMER-HSA-2672351
Cardiac conductionREACTOMER-HSA-5576891
Ion homeostasisREACTOMER-HSA-5578775

Protein levels (Protein atlas)

Not detected
Low
Medium
High

PharmGKB

Entity IDNameTypeEvidenceAssociationPKPDPMIDs
PA451906warfarinChemicalClinicalAnnotationassociatedPD27488176

References

Pubmed IDYearTitleCitations
368977572023Overexpression of ASPH protein predicts poor outcomes in retroperitoneal liposarcoma patients.0
371321012023Aspartate β-hydroxylase (ASPH) Accelerates Intrahepatic Cholangiocarcinoma Metastasis via Upregulating SHH Signaling Pathway.0
368977572023Overexpression of ASPH protein predicts poor outcomes in retroperitoneal liposarcoma patients.0
371321012023Aspartate β-hydroxylase (ASPH) Accelerates Intrahepatic Cholangiocarcinoma Metastasis via Upregulating SHH Signaling Pathway.0
359180382022Traboulsi syndrome caused by mutations in ASPH: An autosomal recessive disorder with overlapping features of Marfan syndrome.2
359180382022Traboulsi syndrome caused by mutations in ASPH: An autosomal recessive disorder with overlapping features of Marfan syndrome.2
332518832021A novel mutation in the aspartate beta-hydroxylase (ASPH) gene is associated with a rare form of Traboulsi syndrome.0
338870992021Human Oxygenase Variants Employing a Single Protein Fe(II) Ligand Are Catalytically Active.8
340188982021Expanding the clinical spectrum and management of Traboulsi syndrome: report on two siblings homozygous for a novel pathogenic variant in ASPH.3
344331812021Overexpression of Human Aspartyl (Asparaginyl) β-hydroxylase in NSCLC: Its Diagnostic Value by Means of Exosomes of Bronchoalveolar Lavage.3
332518832021A novel mutation in the aspartate beta-hydroxylase (ASPH) gene is associated with a rare form of Traboulsi syndrome.0
338870992021Human Oxygenase Variants Employing a Single Protein Fe(II) Ligand Are Catalytically Active.8
340188982021Expanding the clinical spectrum and management of Traboulsi syndrome: report on two siblings homozygous for a novel pathogenic variant in ASPH.3
344331812021Overexpression of Human Aspartyl (Asparaginyl) β-hydroxylase in NSCLC: Its Diagnostic Value by Means of Exosomes of Bronchoalveolar Lavage.3
321073122020Kinetic parameters of human aspartate/asparagine-β-hydroxylase suggest that it has a possible function in oxygen sensing.17

Citation

Dessen P

ASPH (aspartate beta-hydroxylase)

Atlas Genet Cytogenet Oncol Haematol. 2003-02-01

Online version: http://atlasgeneticsoncology.org/gene/716/asph-(aspartate-beta-hydroxylase)