PDE6B (phosphodiesterase 6B)

2014-11-01  

Identity

HGNC
LOCATION
4p16.3
LOCUSID
ALIAS
CSNB3,CSNBAD2,GMP-PDEbeta,PDEB,RP40,rd1
FUSION GENES

Other Information

Locus ID:

NCBI: 5158
MIM: 180072
HGNC: 8786
Ensembl: ENSG00000133256

Variants:

dbSNP: 5158
ClinVar: 5158
TCGA: ENSG00000133256
COSMIC: PDE6B

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000133256ENST00000255622P35913
ENSG00000133256ENST00000429163P35913
ENSG00000133256ENST00000461490H7C4F7
ENSG00000133256ENST00000465426C9J628
ENSG00000133256ENST00000471824H7C4P9
ENSG00000133256ENST00000487902C9J7V6
ENSG00000133256ENST00000496514P35913

Expression (GTEx)

0
5
10
15
20
25

Pathways

PathwaySourceExternal ID
Purine metabolismKEGGko00230
Purine metabolismKEGGhsa00230
PhototransductionKEGGko04744
PhototransductionKEGGhsa04744
Signal TransductionREACTOMER-HSA-162582
Signaling by WntREACTOMER-HSA-195721
Beta-catenin independent WNT signalingREACTOMER-HSA-3858494
Ca2+ pathwayREACTOMER-HSA-4086398
Visual phototransductionREACTOMER-HSA-2187338
The phototransduction cascadeREACTOMER-HSA-2514856
Activation of the phototransduction cascadeREACTOMER-HSA-2485179
Inactivation, recovery and regulation of the phototransduction cascadeREACTOMER-HSA-2514859

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
369595492023A novel homozygous missense substitution p.Thr313Ile in the PDE6B gene underlies autosomal recessive retinitis pigmentosa in a consanguineous Pakistani family.1
370945572023A Novel Intronic Deletion in PDE6B Causes Autosomal Recessive Retinitis Pigmentosa by Interfering with RNA Splicing.0
369595492023A novel homozygous missense substitution p.Thr313Ile in the PDE6B gene underlies autosomal recessive retinitis pigmentosa in a consanguineous Pakistani family.1
370945572023A Novel Intronic Deletion in PDE6B Causes Autosomal Recessive Retinitis Pigmentosa by Interfering with RNA Splicing.0
341705012022Photoreceptor Phosphodiesterase (PDE6): Structure, Regulatory Mechanisms, and Implications for Treatment of Retinal Diseases.8
350330392022Novel variants in PDE6A and PDE6B genes and its phenotypes in patients with retinitis pigmentosa in Chinese families.3
363760652022Identification of a novel large multigene deletion and a frameshift indel in PDE6B as the underlying cause of early-onset recessive rod-cone degeneration.0
341705012022Photoreceptor Phosphodiesterase (PDE6): Structure, Regulatory Mechanisms, and Implications for Treatment of Retinal Diseases.8
350330392022Novel variants in PDE6A and PDE6B genes and its phenotypes in patients with retinitis pigmentosa in Chinese families.3
363760652022Identification of a novel large multigene deletion and a frameshift indel in PDE6B as the underlying cause of early-onset recessive rod-cone degeneration.0
336334362021Clinical and genetic investigations of three Moroccan families with retinitis pigmentosa phenotypes.1
336735122021Clinical Phenotype of PDE6B-Associated Retinitis Pigmentosa.7
345840502021PDE6B Mutation-associated Inherited Retinal Disease.1
336334362021Clinical and genetic investigations of three Moroccan families with retinitis pigmentosa phenotypes.1
336735122021Clinical Phenotype of PDE6B-Associated Retinitis Pigmentosa.7

Citation

Dessen P

PDE6B (phosphodiesterase 6B)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/71795/pde6b-(phosphodiesterase-6b)