PDE6D (phosphodiesterase 6D)

2014-11-01  

Identity

HGNC
LOCATION
2q37.1
LOCUSID
ALIAS
JBTS22,PDED
FUSION GENES

Other Information

Locus ID:

NCBI: 5147
MIM: 602676
HGNC: 8788
Ensembl: ENSG00000156973

Variants:

dbSNP: 5147
ClinVar: 5147
TCGA: ENSG00000156973
COSMIC: PDE6D

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000156973ENST00000287600O43924
ENSG00000156973ENST00000287600Q6IB24
ENSG00000156973ENST00000409772B8ZZK5
ENSG00000156973ENST00000428104C9IZ52

Expression (GTEx)

0
10
20
30
40
50
60
70

Pathways

PathwaySourceExternal ID
Purine metabolismKEGGko00230
Purine metabolismKEGGhsa00230
Organelle biogenesis and maintenanceREACTOMER-HSA-1852241
Cilium AssemblyREACTOMER-HSA-5617833
Cargo trafficking to the periciliary membraneREACTOMER-HSA-5620920
ARL13B-mediated ciliary trafficking of INPP5EREACTOMER-HSA-5624958

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
366722472023PDE6D Mediates Trafficking of Prenylated Proteins NIM1K and UBL3 to Primary Cilia.1
366722472023PDE6D Mediates Trafficking of Prenylated Proteins NIM1K and UBL3 to Primary Cilia.1
354220652022Validation of a small molecule inhibitor of PDE6D-RAS interaction with favorable anti-leukemic effects.2
354220652022Validation of a small molecule inhibitor of PDE6D-RAS interaction with favorable anti-leukemic effects.2
304234422019A novel PDE6D mutation in a patient with Joubert syndrome type 22 (JBTS22).3
304234422019A novel PDE6D mutation in a patient with Joubert syndrome type 22 (JBTS22).3
279117092016Shuttling and sorting lipid-modified cargo into the cilia.14
281729802016Prenylated retinal ciliopathy protein RPGR interacts with PDE6δ and regulates ciliary localization of Joubert syndrome-associated protein INPP5E.21
279117092016Shuttling and sorting lipid-modified cargo into the cilia.14
281729802016Prenylated retinal ciliopathy protein RPGR interacts with PDE6δ and regulates ciliary localization of Joubert syndrome-associated protein INPP5E.21
241668462014A homozygous PDE6D mutation in Joubert syndrome impairs targeting of farnesylated INPP5E protein to the primary cilium.73
241668462014A homozygous PDE6D mutation in Joubert syndrome impairs targeting of farnesylated INPP5E protein to the primary cilium.73
235590672013The interplay between RPGR, PDEδ and Arl2/3 regulate the ciliary targeting of farnesylated cargo.42
235590672013The interplay between RPGR, PDEδ and Arl2/3 regulate the ciliary targeting of farnesylated cargo.42
231505592012ARL13B, PDE6D, and CEP164 form a functional network for INPP5E ciliary targeting.134

Citation

Dessen P

PDE6D (phosphodiesterase 6D)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/71797/pde6d-(phosphodiesterase-6d)