RARS2 (arginyl-tRNA synthetase 2, mitochondrial)

2014-11-01  

Identity

HGNC
LOCATION
6q15
LOCUSID
ALIAS
ArgRS,DALRD2,PCH6,PRO1992,RARSL
FUSION GENES

Other Information

Locus ID:

NCBI: 57038
MIM: 611524
HGNC: 21406
Ensembl: ENSG00000146282

Variants:

dbSNP: 57038
ClinVar: 57038
TCGA: ENSG00000146282
COSMIC: RARS2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000146282ENST00000369536Q5T160
ENSG00000146282ENST00000451155H0Y450

Expression (GTEx)

0
5
10
15
20
25
30
35
40
45
50

Pathways

PathwaySourceExternal ID
Aminoacyl-tRNA biosynthesisKEGGko00970
Aminoacyl-tRNA biosynthesisKEGGhsa00970
Aminoacyl-tRNA biosynthesis, eukaryotesKEGGhsa_M00359
Aminoacyl-tRNA biosynthesis, eukaryotesKEGGM00359
Gene ExpressionREACTOMER-HSA-74160
tRNA AminoacylationREACTOMER-HSA-379724
Mitochondrial tRNA aminoacylationREACTOMER-HSA-379726

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
380092862024Clinical and genetic analysis of infants with pontocerebellar hypoplasia type 6 caused by RARS2 variations.1
380092862024Clinical and genetic analysis of infants with pontocerebellar hypoplasia type 6 caused by RARS2 variations.1
354683442022Novel RARS2 Variants: Updating the Diagnosis and Pathogenesis of Pontocerebellar Hypoplasia Type 6.2
354683442022Novel RARS2 Variants: Updating the Diagnosis and Pathogenesis of Pontocerebellar Hypoplasia Type 6.2
327256322020Whole-exome sequencing in adult patients with developmental and epileptic encephalopathy: It is never too late.14
327256322020Whole-exome sequencing in adult patients with developmental and epileptic encephalopathy: It is never too late.14
269709472016RARS2 mutations cause early onset epileptic encephalopathy without ponto-cerebellar hypoplasia.13
277692812016Novel homozygous RARS2 mutation in two siblings without pontocerebellar hypoplasia - further expansion of the phenotypic spectrum.16
269709472016RARS2 mutations cause early onset epileptic encephalopathy without ponto-cerebellar hypoplasia.13
277692812016Novel homozygous RARS2 mutation in two siblings without pontocerebellar hypoplasia - further expansion of the phenotypic spectrum.16
258099392015A novel mutation in the promoter of RARS2 causes pontocerebellar hypoplasia in two siblings.18
258099392015A novel mutation in the promoter of RARS2 causes pontocerebellar hypoplasia in two siblings.18
225695812013Pontocerebellar hypoplasia type 6 caused by mutations in RARS2: definition of the clinical spectrum and molecular findings in five patients.41
225695812013Pontocerebellar hypoplasia type 6 caused by mutations in RARS2: definition of the clinical spectrum and molecular findings in five patients.41
220866042012Further delineation of pontocerebellar hypoplasia type 6 due to mutations in the gene encoding mitochondrial arginyl-tRNA synthetase, RARS2.24

Citation

Dessen P

RARS2 (arginyl-tRNA synthetase 2, mitochondrial)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/72491/rars2-(arginyl-trna-synthetase-2-mitochondrial)