RSPH4A (radial spoke head component 4A)

2014-11-01  

Identity

HGNC
LOCATION
6q22.1
LOCUSID
ALIAS
CILD11,RSHL3,RSPH6B,dJ412I7.1

Other Information

Locus ID:

NCBI: 345895
MIM: 612647
HGNC: 21558
Ensembl: ENSG00000111834

Variants:

dbSNP: 345895
ClinVar: 345895
TCGA: ENSG00000111834
COSMIC: RSPH4A

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000111834ENST00000229554Q5TD94
ENSG00000111834ENST00000368580Q5TD94
ENSG00000111834ENST00000368581Q5TD94

Expression (GTEx)

0
1
2
3
4
5
6
7
8
9
10

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
367682592023The RSPH4A Gene in Primary Ciliary Dyskinesia.4
367682592023The RSPH4A Gene in Primary Ciliary Dyskinesia.4
338523482021Structural insights into the cause of human RSPH4A primary ciliary dyskinesia.10
338523482021Structural insights into the cause of human RSPH4A primary ciliary dyskinesia.10
289392162018A targeted next-generation sequencing panel reveals novel mutations in Japanese patients with primary ciliary dyskinesia.16
289392162018A targeted next-generation sequencing panel reveals novel mutations in Japanese patients with primary ciliary dyskinesia.16
257895482015Immunofluorescence Analysis and Diagnosis of Primary Ciliary Dyskinesia with Radial Spoke Defects.59
257895482015Immunofluorescence Analysis and Diagnosis of Primary Ciliary Dyskinesia with Radial Spoke Defects.59
237980572013Founder mutation in RSPH4A identified in patients of Hispanic descent with primary ciliary dyskinesia.32
237980572013Founder mutation in RSPH4A identified in patients of Hispanic descent with primary ciliary dyskinesia.32
224482642012Mutations in radial spoke head genes and ultrastructural cilia defects in East-European cohort of primary ciliary dyskinesia patients.30
224482642012Mutations in radial spoke head genes and ultrastructural cilia defects in East-European cohort of primary ciliary dyskinesia patients.30

Citation

Dessen P

RSPH4A (radial spoke head component 4A)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/72911/rsph4a-(radial-spoke-head-component-4a)