SUCLA2 (succinate-CoA ligase ADP-forming subunit beta)

2014-11-01  

Identity

HGNC
LOCATION
13q14.2
LOCUSID
ALIAS
A-BETA,A-SCS,LINC00444,MTDPS5,SCS-betaA
FUSION GENES

Other Information

Locus ID:

NCBI: 8803
MIM: 603921
HGNC: 11448
Ensembl: ENSG00000136143

Variants:

dbSNP: 8803
ClinVar: 8803
TCGA: ENSG00000136143
COSMIC: SUCLA2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000136143ENST00000433022Q5T9Q8
ENSG00000136143ENST00000434484Q5T9Q5
ENSG00000136143ENST00000470760A0A0U1RQF8
ENSG00000136143ENST00000493152A0A0U1RQL1
ENSG00000136143ENST00000497202A0A0U1RQU7
ENSG00000136143ENST00000634878A0A0U1RRI1
ENSG00000136143ENST00000642944A0A2R8YDQ9
ENSG00000136143ENST00000643023A0A2R8Y6Y7
ENSG00000136143ENST00000643246A0A2R8YF84
ENSG00000136143ENST00000643584Q9P2R7
ENSG00000136143ENST00000643584E5KS60
ENSG00000136143ENST00000644338A0A2R8Y5P6
ENSG00000136143ENST00000646602A0A2R8Y6E6
ENSG00000136143ENST00000646804A0A2R8YDQ9
ENSG00000136143ENST00000646932Q9P2R7
ENSG00000136143ENST00000646932E5KS60
ENSG00000136143ENST00000647361A0A2R8Y5P4

Expression (GTEx)

0
10
20
30
40
50
60
70

Pathways

PathwaySourceExternal ID
Citrate cycle (TCA cycle)KEGGko00020
Propanoate metabolismKEGGko00640
Citrate cycle (TCA cycle)KEGGhsa00020
Propanoate metabolismKEGGhsa00640
Metabolic pathwaysKEGGhsa01100
Citrate cycle, second carbon oxidation, 2-oxoglutarate => oxaloacetateKEGGhsa_M00011
Citrate cycle (TCA cycle, Krebs cycle)KEGGM00009
Citrate cycle, second carbon oxidation, 2-oxoglutarate => oxaloacetateKEGGM00011
Carbon metabolismKEGGhsa01200
Carbon metabolismKEGGko01200
Citrate cycle (TCA cycle, Krebs cycle)KEGGhsa_M00009
MetabolismREACTOMER-HSA-1430728
The citric acid (TCA) cycle and respiratory electron transportREACTOMER-HSA-1428517
Pyruvate metabolism and Citric Acid (TCA) cycleREACTOMER-HSA-71406
Citric acid cycle (TCA cycle)REACTOMER-HSA-71403

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
332313682021SUCLA2 Arg407Trp mutation can cause a nonprogressive movement disorder - deafness syndrome.4
339914852021SUCLA2-coupled regulation of GLS succinylation and activity counteracts oxidative stress in tumor cells.60
332313682021SUCLA2 Arg407Trp mutation can cause a nonprogressive movement disorder - deafness syndrome.4
339914852021SUCLA2-coupled regulation of GLS succinylation and activity counteracts oxidative stress in tumor cells.60
326946112020Pharmacologically targetable vulnerability in prostate cancer carrying RB1-SUCLA2 deletion.7
332301812020SUCLA2 mutations cause global protein succinylation contributing to the pathomechanism of a hereditary mitochondrial disease.27
326946112020Pharmacologically targetable vulnerability in prostate cancer carrying RB1-SUCLA2 deletion.7
332301812020SUCLA2 mutations cause global protein succinylation contributing to the pathomechanism of a hereditary mitochondrial disease.27
287490332017Co-occurring Down syndrome and SUCLA2-related mitochondrial depletion syndrome.0
287490332017Co-occurring Down syndrome and SUCLA2-related mitochondrial depletion syndrome.0
264755972016Succinate-CoA ligase deficiency due to mutations in SUCLA2 and SUCLG1: phenotype and genotype correlations in 71 patients.35
268636012016Influences of XDH genotype by gene-gene interactions with SUCLA2 for thiopurine-induced leukopenia in Korean patients with Crohn's disease.5
274843062016Expanding the phenotypic spectrum of Succinyl-CoA ligase deficiency through functional validation of a new SUCLG1 variant.8
277666102016Knockdown of Sucla2 decreases the viability of mouse spermatocytes by inducing apoptosis through injury of the mitochondrial function of cells.1
264755972016Succinate-CoA ligase deficiency due to mutations in SUCLA2 and SUCLG1: phenotype and genotype correlations in 71 patients.35

Citation

Dessen P

SUCLA2 (succinate-CoA ligase ADP-forming subunit beta)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/74351/sucla2-(succinate-coa-ligase-adp-forming-subunit-beta)