TTC21B (tetratricopeptide repeat domain 21B)

2014-11-01  

Identity

HGNC
LOCATION
2q24.3
LOCUSID
ALIAS
ATD4,FAP60,FLA17,IFT139,IFT139B,JBTS11,NPHP12,Nbla10696,SRTD4,THM1
FUSION GENES

Other Information

Locus ID:

NCBI: 79809
MIM: 612014
HGNC: 25660
Ensembl: ENSG00000123607

Variants:

dbSNP: 79809
ClinVar: 79809
TCGA: ENSG00000123607
COSMIC: TTC21B

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000123607ENST00000243344Q7Z4L5
ENSG00000123607ENST00000392695H9KV93
ENSG00000123607ENST00000652557A0A494C0N4

Expression (GTEx)

0
5
10
15
20
25

Pathways

PathwaySourceExternal ID
Organelle biogenesis and maintenanceREACTOMER-HSA-1852241
Cilium AssemblyREACTOMER-HSA-5617833
Intraflagellar transportREACTOMER-HSA-5620924
Signal TransductionREACTOMER-HSA-162582
Signaling by HedgehogREACTOMER-HSA-5358351
Hedgehog 'off' stateREACTOMER-HSA-5610787

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
384395782024Clinical report and genetic analysis of rare premature infant nephronophthisis caused by biallelic TTC21B variants.1
384395782024Clinical report and genetic analysis of rare premature infant nephronophthisis caused by biallelic TTC21B variants.1
356959662023Lethal neonatal respiratory failure due to biallelic variants in BBS1 and monoallelic variant in TTC21B.1
356959662023Lethal neonatal respiratory failure due to biallelic variants in BBS1 and monoallelic variant in TTC21B.1
362732012022Biallelic mutations of TTC12 and TTC21B were identified in Chinese patients with multisystem ciliopathy syndromes.3
362732012022Biallelic mutations of TTC12 and TTC21B were identified in Chinese patients with multisystem ciliopathy syndromes.3
335477612021A novel heterotaxy gene: Expansion of the phenotype of TTC21B-spectrum disease.4
335991922021Retinal dystrophy as part of TTC21B-associated ciliopathy.1
335477612021A novel heterotaxy gene: Expansion of the phenotype of TTC21B-spectrum disease.4
335991922021Retinal dystrophy as part of TTC21B-associated ciliopathy.1
281244832018Mutations in TTC21B cause different phenotypes in two childhood cases in China.12
281244832018Mutations in TTC21B cause different phenotypes in two childhood cases in China.12
269401252017Contribution of the TTC21B gene to glomerular and cystic kidney diseases.23
269401252017Contribution of the TTC21B gene to glomerular and cystic kidney diseases.23
269255472016Expanding the phenotype of CRB2 mutations - A new ciliopathy syndrome?11

Citation

Dessen P

TTC21B (tetratricopeptide repeat domain 21B)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/75272/chromosome-explorer/new-content/