CPLANE1 (ciliogenesis and planar polarity effector 1)

2018-11-01  

Identity

HGNC
LOCATION
5p13.2
LOCUSID
ALIAS
C5orf42,Hug,JBTS17,OFD6

Other Information

Locus ID:

NCBI: 65250
MIM: 614571
HGNC: 25801
Ensembl: ENSG00000197603

Variants:

dbSNP: 65250
ClinVar: 65250
TCGA: ENSG00000197603
COSMIC: CPLANE1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000197603ENST00000425232Q9H799
ENSG00000197603ENST00000508244Q9H799
ENSG00000197603ENST00000509849H0YA77
ENSG00000197603ENST00000511824R4GNH6
ENSG00000197603ENST00000514429H0Y9I8
ENSG00000197603ENST00000651892A0A494BZW6

References

Pubmed IDYearTitleCitations
350923592022Exome sequencing and RNA analysis identify two novel CPLANE1 variants causing Joubert syndrome.5
350923592022Exome sequencing and RNA analysis identify two novel CPLANE1 variants causing Joubert syndrome.5
335172812021Salivary CPLANE1 Levels as a Biomarker of Oral Squamous Cell Carcinoma.4
338224872021Clinical heterogeneity and intrafamilial variability of Joubert syndrome in two siblings with CPLANE1 variants.5
335172812021Salivary CPLANE1 Levels as a Biomarker of Oral Squamous Cell Carcinoma.4
338224872021Clinical heterogeneity and intrafamilial variability of Joubert syndrome in two siblings with CPLANE1 variants.5
322330902020Four novel compound heterozygous mutations in C5orf42 gene in patients with pure and mild Joubert syndrome.5
323358742020[Genetic testing and prenatal diagnosis for two families affected with Joubert syndrome].0
322330902020Four novel compound heterozygous mutations in C5orf42 gene in patients with pure and mild Joubert syndrome.5
323358742020[Genetic testing and prenatal diagnosis for two families affected with Joubert syndrome].0
310044382019Extraciliary roles of the ciliopathy protein JBTS17 in mitosis and neurogenesis.7
310044382019Extraciliary roles of the ciliopathy protein JBTS17 in mitosis and neurogenesis.7
296056582018Novel mutations in the ciliopathy-associated gene CPLANE1 (C5orf42) cause OFD syndrome type VI rather than Joubert syndrome.11
296056582018Novel mutations in the ciliopathy-associated gene CPLANE1 (C5orf42) cause OFD syndrome type VI rather than Joubert syndrome.11
284316312017Neuroimaging findings in Joubert syndrome with C5orf42 gene mutations: A milder form of molar tooth sign and vermian hypoplasia.12

Citation

Dessen P

CPLANE1 (ciliogenesis and planar polarity effector 1)

Atlas Genet Cytogenet Oncol Haematol. 2018-11-01

Online version: http://atlasgeneticsoncology.org/gene/80380/cplane1-(ciliogenesis-and-planar-polarity-effector-1)