Genetic tumor syndromes involving the thorax

2023-05-12   Paola Dal Cin, PhD 

1.Brigham and Women's Hospital , Harvard Medical School, Boston , MA (USA)

Classification

Definition

Hereditary factors can contribute to the development of thoracic tumors. Constitutional pathogenic variants can now be routinely screened by next generation sequencing (NGS) to identify at-risk individuals in affected families and offer genetic counseling, choice of therapy and surveillance guideline. There is a wide range of hereditary genetic disorders that are associated with familiar predisposition to a variety of thoracic neoplasms.  See details in WHO 2020 Thoracic Tumours.

Genetic tumor syndromes involving the thorax
Li-Fraumeni syndrome OMIM:151623
BAP1 tumor predispositon syndrome OMIM:614327
Carney complex , type 1OMIM:160980
DICER1 syndromeOMIM:601200
Tuberous sclerosisOMIM:191100, OMIM:613254
Gorlin syndromeOMIM:109400
Gardner syndrome OMIM:175100
Neurofibromatosis type 1OMIM:16200
Neurofibromatosis type 2OMIM:10100
Germline SMARCB1 or LZTR1 mutationsOMIM:609322 or OMIM:600574
Multiple endocrine neoplasia type 2 OMIM:171400
Von Hippel -Lindau syndromeOMIM:193300
Hereditary paraganglioma-pheochromocytoma syndromeOMIM:115310
Carney-Stratakis syndromeOMIM:606864
Peutz-Jeghers syndrome OMIM:175200
Germline EGFRp.T790M1-3
ERBB2 germline mutation4,5

Article Bibliography

Reference NumberPubmed IDLast YearTitleAuthors
1247360662014Hereditary lung cancer syndrome targets never smokers with germline EGFR gene T790M mutations.Gazdar A et al
2225881502012Polychlorinated biphenyls (PCBs) analysis using a miniaturized high-resolution time-of-flight mass spectrometer "MULTUM-S II".Shimma S et al
3345900052021Genomic Evolution in a Patient With Lung Adenocarcinoma With a Germline EGFR T790M Mutation.Mäkinen N et al
4306109262019EGFR and ERBB2 Germline Mutations in Chinese Lung Cancer Patients and Their Roles in Genetic Susceptibility to Cancer.Lu S et al
5342749692021Germline ERBB3 mutation in familial non-small-cell lung carcinoma: expanding ErbB's role in oncogenesis.McInerney-Leo AM et al

Citation

Paola Dal Cin, PhD

Genetic tumor syndromes involving the thorax

Atlas Genet Cytogenet Oncol Haematol. 2023-05-12

Online version: http://atlasgeneticsoncology.org/solid-tumor/209136/genetic-tumor-syndromes-involving-the-thorax