Nasal, paranasal and skull base tumors

2025-07-17   Paola Dal Cin, PhD 

1.Brigham and Women's Hospital , Harvard Medical School, Boston , MA (USA)

Classification

Definition

There are several entities that occur exclusively or predominantly in the sinonasal tract region and demonstrate a diverse genetic landscape and varying clinical courses. 1-3 Genetic studies, as well as, the availability of more specific and sensitive immunohistochemical antibodies have led to better understanding and more accurate classification of the lesions in the sinonasal tract region , based on specific genetic alterations e.g., DEK::AFF2, BRD4::NUTM1  ETV6::NTRK3. PAX3::MAML3, protein expression e.g., Beta-catenin, specific gene mutation e.g., CTNNB1, IDH2, SMARCB1, SMARCA4, TBXT, BRAF or infection by oncogenic viruses e.g., EBV, HPV. 4,5

Article Bibliography

Reference NumberPubmed IDLast YearTitleAuthors
1327254352020Novel Biomarkers in Sinonasal Cancers: from Bench to Bedside.Lechner M et al
2353129762022Update from the 5th Edition of the World Health Organization Classification of Head and Neck Tumors: Nasal Cavity, Paranasal Sinuses and Skull Base.Thompson LDR et al
3375917732023Update from the 5th Edition of the WHO Classification of Nasal, Paranasal, and Skull Base Tumors: Imaging Overview with Histopathologic and Genetic Correlation.Agarwal A et al
4367530242023Translocations and Gene Fusions in Sinonasal Malignancies.Larkin R et al
5384912282024Molecularly defined sinonasal malignancies: an overview with focus on the current WHO classification and recently described provisional entities.Skálová A et al

Citation

Paola Dal Cin, PhD

Nasal, paranasal and skull base tumors

Atlas Genet Cytogenet Oncol Haematol. 2025-07-17

Online version: http://atlasgeneticsoncology.org/solid-tumor/209324/nasal-paranasal-and-skull-base-tumors