Diffuse idiopathic neuroendocrine cell hyperplasia

2023-05-16   Paola Dal Cin, PhD , Yin (Rex) Hung, MD 

1.Brigham and Women's Hospital , Harvard Medical School, Boston , MA (USA)
2.Massachussetts General Hospital,Harvard Medical School, Boston (MA)

Classification

Definition

Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) is a rare premalignant condition that can transform into carcinoid tumors. 1,2 No gene alterations reported in EGFR, KRAS, KIT, PDGFRB genes, MET, or ALK have been so far reported. 3

Article Bibliography

Reference NumberPubmed IDLast YearTitleAuthors
1339271312021Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia: DIPNECH.Almquist DR et al
2347950352022Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia: clinical characteristics and progression to carcinoid tumour.Sun TY et al
3294381702018Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia (DIPNECH) Syndrome and Carcinoid Tumors With/Without NECH: A Clinicopathologic, Radiologic, and Immunomolecular Comparison Study.Mengoli MC et al

Citation

Paola Dal Cin, PhD ; Yin (Rex) Hung, MD

Diffuse idiopathic neuroendocrine cell hyperplasia

Atlas Genet Cytogenet Oncol Haematol. 2023-05-16

Online version: http://atlasgeneticsoncology.org/solid-tumor/209147/diffuse-idiopathic-neuroendocrine-cell-hyperplasia